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Melanosis Neurocutanea

definition

Rare condition characterized by extensive congenital hairy nevocytic nevi, often in the bathing trunk region, a dense scattering of smaller, pigmented nevocytic nevi, especially on the palms and soles, and similar aggregations of pigment-forming naevus cells in the meninges, brain, and spinal cord. Complications arise from the development of an obstructive internal hydrocephalus. A metastasising melanoma may also arise in the skin or CNS, accounting for the poor prognosis of the disorder.

synonyms

Melanosis Neurocutanea, Melanoblastosis Neurocutanea Touraine, Neurocutaneous Melanosis

Images

13 images found for this diagnose
localisation: shoulder region, diagnosis: Melanosis Neurocutanea localisation: flank, buttocks, diagnosis: Melanosis Neurocutanea localisation: back, buttocks, diagnosis: Melanosis Neurocutanea localisation: abdomen, back, lower back, buttocks, arms, legs, upper leg, diagnosis: Melanosis Neurocutanea localisation: abdomen, upper leg, diagnosis: Melanosis Neurocutanea localisation: abdomen, buttocks, diagnosis: Melanosis Neurocutanea localisation: back, diagnosis: Melanosis Neurocutanea localisation: back, diagnosis: Melanosis Neurocutanea diagnosis: Melanosis Neurocutanea diagnosis: Melanosis Neurocutanea diagnosis: Melanosis Neurocutanea diagnosis: Melanosis Neurocutanea diagnosis: Melanosis Neurocutanea