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Angiokeratoma Corporis Circumscriptum (Fabry)

definition

Vascular malformation characterized by dilation of superficial vessels of the dermis and hyperkeratosis of the overlying epidermis. Lesions present as solitary hyperkeratotic papules or plaques with an uneven verrucous surface, ranging in colour from deep-red to blue-black. Typical areas of involvement are the thighs, lower legs, and buttocks, but lesions may also occur elsewhere. The lesions may be present from birth or develop later on. There is no tendency to spontaneous involution.

synonyms

Angiokeratoma Corporis Circumscriptum (Fabry), Angiokeratoma Corporis Naeviforme, Angiokeratoma Circumscriptum, Haemangioma Verrucosum

UMLS

Angiokeratoma circumscriptum

images

2 images found for this diagnose localisation: lower leg, back of the feet, diagnosis: Angiokeratoma Corporis Circumscriptum (Fabry) localisation: lower leg, diagnosis: Angiokeratoma Corporis Circumscriptum (Fabry)