Suchbegriff

🔎

nach Körperregion

Melanosis neurocutanea

Definition

Rare condition characterized by extensive congenital hairy nevocytic nevi, often in the bathing trunk region, a dense scattering of smaller, pigmented nevocytic nevi, especially on the palms and soles, and similar aggregations of pigment-forming naevus cells in the meninges, brain, and spinal cord. Complications arise from the development of an obstructive internal hydrocephalus. A metastasising melanoma may also arise in the skin or CNS, accounting for the poor prognosis of the disorder.

Synonyme

Melanosis neurocutanea, Neurokutane Melanose, Neurokutanes Melanoblastosesyndrom, Melanoblastosis neurocutanea Touraine

Bilder

2 Bilder für diese Diagnose
Lokalisation: Schulterregion, Diagnose: Melanosis neurocutanea Lokalisation: Bauch, Oberschenkel, Diagnose: Melanosis neurocutanea