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Pityriasis Lichenoides et Varioliformis Acuta (Mucha-Habermann)

definition

Pityriasis lichenoides is an uncommon inflammatory disease of unknown aetiology divided into an acute and a chronic form. Mucha-Habermann disease corresponds to the acute form and is characterised by recurrent erythematous, round papules, hemorrhage, blisters and varioliform vesiculopustules. The distribution of the lesions is variable, the scalp, hands and feet being seldom involved. There may be just a few episodes and complete resolution within 6-8 week, but lesions may also recur over many months or even years. The chronic form of the disease is called pityriasis lichenoides chronica.

synonyms

Pityriasis Lichenoides et Varioliformis Acuta (Mucha-Habermann), Mucha Habermann Disease, Acute Guttate Parapsoriasis

UMLS

Acute lichenoid pityriasis, Acute parapsoriasis, Acute Pityriasis Lichenoides, Acute vasculitic parapsoriasis, Disease, Mucha-Habermann, Mucha Habermann Disease, Mucha-Habermann Disease, Parapsoriasis varioliformis acuta, Pityr lichenoid + variol acuta, Pityriasis lichenoides acuta, Pityriasis Lichenoides et Varioliformis Acuta, Pityriasis Lichenoides, Acute, PLA - Pityrias lichenoid acuta, PLA - Pityriasis lichenoides acuta, PLEVA - Pit lich + variol acut, PLEVA - Pityriasis lichenoides et varioliformis acuta

Images

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localisation: buttocks, diagnosis: Pityriasis Lichenoides et Varioliformis Acuta (Mucha-Habermann) localisation: buttocks, diagnosis: Pityriasis Lichenoides et Varioliformis Acuta (Mucha-Habermann)