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Pfeifer-Weber-Christian Syndrome

definition

A form of panniculitis characterized by recurrent episodes of fever accompanied by the eruption of single or multiple erythematous subcutaneous nodules on the lower extremities. They normally resolve, but tend to leave depressions in the skin. The condition is most often seen in women, alone or in association with other disorders.

synonyms

Pfeifer-Weber-Christian Syndrome, Weber-Christian Disease, Panniculitis Nodularis Nonsuppurativa et Recidivans

UMLS

Christian-Weber disease, Disease, Christian-Weber, Disease, Weber-Christian, Nod non-supp febr panniculitis, Nodular non-suppurative febrile panniculitis, Nodular Nonsuppurative Panniculitides, Nodular Nonsuppurative Panniculitis, Nonsuppurative Panniculitides, Nodular, Nonsuppurative Panniculitis, Nodular, Panniculitides, Nodular Nonsuppurative, Panniculitis, Nodular Nonsuppurative, Panniculitis, nodular, nonsuppurative, Panniculitis, non-suppurative relapsing nodular, PFEIFFER-WEBER-CHRISTIAN SYNDROME, Relapsing febrile nodular nonsuppurative panniculitis, Relapsing panniculitis, Systemic nodular panniculitis, Weber Christian Disease, Weber Christian panniculitis, Weber-Christian Disease, Weber-Kindler syndrome