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Connective Tissue Nevus

definition

Localized malformation of dermal collagen, elastic fibres, or glycosaminoglycans. Connective tissue nevi are usually seen in young children as firm, clustered, slightly raised, pea-sized, skin-coloured oval lesions, distributed over the abdomen, back, buttocks, arms, or thighs. They form a characteristic component of a number of inherited disorders such as tuberous sclerosis, but may also occur as isolated lesions without any identifiable genetic basis.

synonyms

Connective Tissue Nevus, Cobblestone Nevus

UMLS

Connective tissue nevus, Connective tissue nevus, NOS, Elastoma juvenile, Juvenile elastoma, Nevus elasticus of Lewandowsky, Nevus elasticus vascularis

Images

3 images found for this diagnose
diagnosis: Connective Tissue Nevus diagnosis: Connective Tissue Nevus diagnosis: Connective Tissue Nevus