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Perforating Elastoma

definition

Dermatosis occurring either as an isolated genetic trait with autosomal dominant inheritance or together with connective tissue disorders such as Ehlers-Danlos syndrome, Marfan’s syndrome and osteogenesis imperfecta. In this dermatosis, transepidermal extrusion of elastic material occurs, frequently peri- or transfollicularly. The disorder presents with annular, circular, serpiginous, ridged lesions consisting of narrow, hard, keratotic or verruciform reddish papules. The lesions show a tendency to peripheral progression and central healing. The neck, the cheeks, and the extremities are particularly involved. Perforating Elastoma mainly begins in youth.

synonyms

Perforating Elastoma, Elastosis Perforans Serpiginosa, Elastosis Intrapapillare Perforans Verucciforme, Perforating Serpiginous Elastosis

UMLS

Disease, Lutz-Miescher, Elastoma, Miescher's, Elastosis perforan serpiginosa, Elastosis perforans serpiginosa, Elastosis, perforans serpiginosa, Keratosis follicul serpiginosa, Keratosis follicularis serpiginosa, LUTZ-MIESCHER DISEASE, Miescher's elastoma, Perforat serpiginous elastosis, Perforating elastoma, PERFORATING ELASTOSIS, Perforating serpiginous elastosis

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